Scleromyxedema Problem in Odontological Practice

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Albertas Kriauciunas
Alvydas Gleiznys

Abstract

Scleromyxedema is a skin disorder, which is considered very rare. Its symptoms are mucin accumulation in the patients’ skin, which is also called mucinosis. It causes papular and sclerodermoid bumps. Also, people affected by this disease have increased production of fibroblasts in the absence of a thyroid disorder. Another symptom includes monoclonal gammopathy, which is shown as abnormal protein existence in the person’s blood. This disease has no standard treatment. All patients should have their life quality improved by any means possible. These ses are extremely challenging for most of the treatments, that are being made by a dentist, because the patient is unable to open his mouth wide enough, so that standard dental manipulations can be made. A 60-year-old patient was presented with Scleromyxedema to our clinic. He was unable to open his mouth by more than 1,7 centimeters, which is considered a very narrow mouth opening. Patients face muscles were rigid, especially – musculus orbicularis oris and musculus masseter. Any attempts to open the mouth by more than 1,7 centimeters resulted with ruptures in patients mouth corners. Intra-oral Examination revealed 2 teeth left in the lower jaw, and no teeth in the upper jaw. Patient was in need of masticatory function rehabilitation, phonetics and aesthetics improvement. Such case requires special procedures and specific adaptation, compared to a standard edentulous patients’ treatment. In this case report, we review all the intra oral procedures, which should be modified accordingly to this rare case. Clinicians should be informed of such rare diseases and should be able to diagnose and treat them accordingly.

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How to Cite
Kriauciunas, A., & Gleiznys, A. (2019). Scleromyxedema Problem in Odontological Practice. International Journal for Innovation Education and Research, 7(5), 232-237. https://doi.org/10.31686/ijier.Vol7.Iss5.1502
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References

1. Liotta, Elizabeth A. “Lichen Myxedematosus.” Medscape, 2019, emedicine.medscape.com/article/1074545-overview.
2. Rongioletti F, Rebora A. Mucinoses. Dermatology, VOL. 1, 3rd edn. Elsevier, Philadelphia, 2012: 687.
3. Rongioletti F. Lichen Myxedematosus (papular mucinosis): new concepts and perspectives for an old disease. Semin Cutan Med Surg 2006; 25: 100–104.
4. Pipa S, Sá J, Mondragão A, et al. Scleromyxoedema: the importance of physical examination Case Reports 2018.
URL: https://casereports.bmj.com/content/2018/bcr-2018-227144.long
5. Fleming KE, Virmani D, Sutton E et al. Scleromyxedema and the dermato‐neuro syndrome: case report and review of the literature. J Cutan Pathol 2012; 39: 508–517.
6. De Simone C, Castriota M, Carbone A, Marini Bettolo P, Pieroni M, Rongioletti F. Cardiomyopathy in scleromyxedema: report of a fatal case. Eur J Dermatol 2010; 20: 852–853.
7. Rongioletti F, Merlo G, Cinotti E et al. Scleromyxedema: a multicenter study of characteristics, comorbidities, course, and therapy in 30 patients. J Am Acad Dermatol 2013; 69: 66–72.
8. Jiyeon J. Kim. Revisiting the Removable Partial Denture. Prosthodontics 2019; 63:263-278.
https://www.sciencedirect.com/science/article/abs/pii/S001185321830096X?via%3Dihub
9. Park MW, Eo MY, Seo BY, Nguyen TTH, Kim SM. Gap arthroplasty with active mouth opening exercises using an interocclusal splint in temporomandibular joint ankylosis patients. Maxillofac Plast Reconstr Surg. 2019;41(1):18. doi:10.1186/s40902-019-0200-x
10. Espinosa A, De Miguel E, Morales C, Fonseca E, Gijón‐Baños J. Scleromyxedema associated with arthritis and myopathy: a case report. Clin Exp Rheumatol 1993 11:545–547.
URL: https://www.ncbi.nlm.nih.gov/pubmed/8275591?dopt=Abstract
11. Helfrich DJ, Walker ER, Martinez AJ, Medsger TA Jr. Scleromyxedema myopathy: case report and review of the literature. Arthritis Rheum 1988; 31:1437–1441.
URL: https://www.ncbi.nlm.nih.gov/pubmed/3056423?dopt=Abstract
12. Dinneen AM, Dicken CH. Scleromyxedema. J Am Acad Dermatol 1995; 33:37–43.
URL: https://www.ncbi.nlm.nih.gov/pubmed/7601944?dopt=Abstract